Objectives: To describe the clinical, radiological, and surgical findings from a patient with a post-surgery diagnosis of Malignant Triton Tumor. Materials and Methods: Information was obtained from electronic medical records. A literature review was performed using the following terms: “Soft Tissue Sarcoma”, “Chest Wall Sarcoma”, and “Malignant Triton Tumor”. Results: We report a patient with a 2-year history of a painless mass measuring 17 x 12 x 18 cm, occupying the thoracic and abdominal regions. Imaging revealed two metastases: one located in the inferior lobe of the right lung and the other in the right adrenal gland. The patient was treated with radiotherapy and underwent complete surgical resection. Discussion: Malignant Triton Tumor is a rare and extremely aggressive type of Malignant Nerve Sheath Tumor. The mean age of presentation is 43 years, and it is more frequent in the male population. The most common site of the disease is the head and neck. Pathological diagnosis is generally made after surgery. Although management strategies for this disease are not well established, complete surgical resection is the most effective treatment, and radiotherapy can optimize overall outcomes.