Introduction: Congenital midline cervical cleft is a rare congenital mid-line anomaly of the neck. There are different theories as to the origins of CMCC. Nevertheless, most believe that is due to impaired fusion of the first and second branchial arches during mesoderm formation. There are less than 100 reported cases in the literature. Case report: A newborn with a mid-line cervical injury without other associated abnormalities. A complete excision of the lesion and the blind-ended sinus were performed and the skin was closed with a Z-plasty approach. Discussion: Congenital mid-line cervical cleft requires early diagnosis, the study of associated abnormalities and an early repair is recommended to aesthetically handle the case and to prevent blind-ended sinus infection.