The von Willebrand disease is a coagulopathy caused by the deficiency of the gene that modifies the organism's ability to produce sufficient factors that promotes coagulation. What is yet unknown by dental surgeons are the means to treat these patients. This patient has au functional abilities, but a coagulation disturbs is observed. It's a normal patient, but he bleeds excessively. The dentist showed always be attentive to the patient's familiar and pathological background, so he can initiate the dental treatment in synergy with the hematologist; who wile program the necessity or not of factor reposition that the patient might need during the treatment. In this article we present a clinical case of von Willebrand disease and we discuss the management odontological of this patient.