Parachordoma is an unusual soft tissue tumour, falling within the mixed tumor/myoepithelioma spectrum. Only 64 cases have been reported since it was first described in 1950; of these 10 occurred in children. The overall age range is broad but the majority of patients are between 40 and 50 years old. Morphologically it is similar to chordoma but with an extraaxial location, occurring most frequently in the proximal limbs. Furthermore, it shows a different pattern with immunostaining. It is a slow growing tumour with local invasion, although metastases have been reported. We present a case of parachordoma in an 8 year old boy who presented with a slow growing mass in his left hand which recurred 6 months post-operatively. © 2011 SEAP y SEC.