Introduction: The retinal astrocytic hamartoma or retinal astrocytoma is a benign and vascularized glial tumor. They are often found in association with congenital diseases such as tuberous sclerosis and neurofibromatosis, and are rarely found independently to any systemic diseases. Case presentation: A male patient, 39 years-old, presents pain and decreased visual acuityin the left eye, clinical picture compatible with acute glaucoma. The ophtalmic examinationshowed angle recession of 180°. Fundus revealed a yellow-gray, upthrust, well delimited solidtumor that was interpreted as retinal astrocytoma. It was decided to monitor tumor progression.Discussion: There are 2 types of retinal astrocytic hamartoma: congenital and acquired, bothsimilar ophthalmoscopically. They may present exudation, cystoid macular edema and adjacentretinal traction. Generally they do not require treatment, but sometimes progressive growthcan occur leading to neovascular glaucoma, pain and blindness.Conclusion: In patients with retinal astrocytic hamartoma diagnosis is imperative to rule outsystemic associations and monitor the tumor growth.