We report a 29 years old woman with a chronic tophaceous gout, whose disease started at the age of 18, On clinical examination, the blood pressure was elevated, The laboratory assessment showed a serum uric acid of 15 mg/dl, a urinary uric acid of 155 mg/24 h, a,creatinine clearance of 59 ml/min/1.73 m(2) and a uric acid excretion fraction off 1.3% (normal 7 to 12%). The clinical and laboratory features of this patient suggest the diagnosis of a familial juvenile gouty nephropathy.